Frontotemporal Demência (FTD) is a group of primary neurodegenerative transtornos primarily affecting the frontal and temporal lobes. Onset is typically insidious com a gradual and worsening course. Several syndromic variants (some com an identified genetic basis or familiality) are described that include presentations com predominantly marked personality and behavioral changes (such as executive dysfunction, apathy, deterioration of social cognition, repetitive behaviours, and dietary changes), predominantly language deficits (that include semantic, agrammatic/nonfluent, and logopenic forms), predominantly movement-related deficits (progressive supranuclear palsy, corticobasal degeneration, multiple systems atrophy, or amyotrophic lateral sclerosis), or a combination of these deficits. Memory function often remains relatively intact, particularly during the early stages of the transtorno.